Beekmans S J, Wiebe M J
Department of Plastic and Reconstructive Surgery at the Vrije Universiteit Medical Center, Amsterdam, the Netherlands.
J Craniofac Surg. 2001 Nov;12(6):569-72. doi: 10.1097/00001665-200111000-00014.
Aplasia cutis is one of the features of the Adams-Oliver syndrome, beside limb anomalies. Aplasia cutis, congenital absence of skin, is a lesion that usually presents over the vertex of the skull. Management of aplasia cutis depends on the size of the skin defect and the child's physical condition. Scalp defects larger than approximately 1 cm should be treated surgically. In patients with aplasia cutis, surgery should preferably be performed using rotation scalp flaps, and additional split skin grafts. The history of two babies with the Adams-Oliver syndrome is presented. In the Adams-Oliver syndrome, large rotation scalp flaps are not reliable due to the abnormal vascularity of the skin. Skin grafting is the safest way, preventing hemorrhage and infection, in the operative treatment of aplasia cutis in these babies.
皮肤发育不全是亚当斯 - 奥利弗综合征的特征之一，此外还有肢体异常。皮肤发育不全，即先天性皮肤缺失，是一种通常出现在头顶的病变。皮肤发育不全的治疗取决于皮肤缺损的大小和患儿的身体状况。大于约1厘米的头皮缺损应进行手术治疗。对于患有皮肤发育不全的患者，手术最好采用旋转头皮瓣，并辅以断层皮片移植。本文介绍了两名患有亚当斯 - 奥利弗综合征婴儿的病例。在亚当斯 - 奥利弗综合征中，由于皮肤血管异常，大型旋转头皮瓣不可靠。在这些婴儿的皮肤发育不全手术治疗中，植皮是预防出血和感染的最安全方法。
