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两例伴有视网膜中央静脉阻塞的霜样树枝状视网膜血管炎

Two cases of frosted branch angiitis with central retinal vein occlusion.

作者信息

Kaburaki T, Nakamura M, Nagasawa K, Nagahara M, Joko S, Fujino Y

机构信息

Department of Ophthalmology, Faculty of Medicine, University of Tokyo, Tokyo, Japan.

出版信息

Jpn J Ophthalmol. 2001 Nov-Dec;45(6):628-33. doi: 10.1016/s0021-5155(01)00416-6.

Abstract

BACKGROUND

Frosted branch angiitis usually occurs in children, and has a good prognosis. We report two cases of unilateral frosted branch angiitis in adults. Both had poor visual outcomes because of associated central retinal vein occlusion and neovascular glaucoma.

CASES

Case 1 was a 36-year-old woman. Almost all retinal veins and some retinal arteries showed vasculitis in her right eye, and veins were slightly dilated and sheathed. Case 2 was a 23-year-old woman. Angle hypopyon was observed in her left eye. Retinal veins were dilated, meandering, and sheathed. Retinal hemorrhages were also observed. In both cases, after systemic steroid therapy the retinal vasculitis gradually decreased, but central retinal vein occlusions gradually developed. Despite systemic administration of urokinase and panretinal photocoagulation, neovascular glaucoma developed, and visual acuity diminished in both cases.

CONCLUSIONS

Two cases of frosted branch angiitis complicated by retinal vein occlusion are reported. Careful observation of retinal blood flow is necessary in frosted branch angiitis in adults.

摘要

背景

霜样树枝状视网膜血管炎通常发生于儿童,预后良好。我们报告两例成人单侧霜样树枝状视网膜血管炎病例。两例患者均因合并视网膜中央静脉阻塞和新生血管性青光眼而视力预后不佳。

病例

病例1为一名36岁女性。其右眼几乎所有视网膜静脉和部分视网膜动脉均出现血管炎,静脉轻度扩张并伴有血管鞘。病例2为一名23岁女性。其左眼可见前房积脓。视网膜静脉扩张、迂曲并伴有血管鞘。还观察到视网膜出血。两例患者经全身类固醇治疗后,视网膜血管炎逐渐减轻,但视网膜中央静脉阻塞逐渐发展。尽管全身应用尿激酶和全视网膜光凝治疗,两例患者均发生了新生血管性青光眼,视力下降。

结论

报告两例霜样树枝状视网膜血管炎合并视网膜静脉阻塞病例。对于成人霜样树枝状视网膜血管炎,有必要仔细观察视网膜血流情况。

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