Borstlap W A, de Wilde P C
Afdeling Mond- en Kaakchirurgie, Academisch Ziekenhuis Nijmegen/St. Radboud, Postbus 9101, 6500 HB Nijmegen.
Ned Tijdschr Tandheelkd. 1999 Apr;106(4):126-7.
Beckwith-Wiedemann syndrome is characterised by variable clinical combinations of exomphalos, macroglossia, gigantism, hypoglycemia and an increased incidence of tumors. This article briefly describes its clinical symptomatology. Recently, hemangiomatous lesions in tongues have been determined.
贝克威思-维德曼综合征的特征是脐膨出、巨舌、巨人症、低血糖和肿瘤发病率增加等多种临床症状组合。本文简要描述其临床症状。最近,已确定舌部存在血管瘤病变。