Ramos M, Dekhili L, Bouchard F, Maurice P
Arch Mal Coeur Vaiss. 1979 Dec;72(12):1382-9.
Atresia of the pulmonary valve with an intact interventricular septum is a rare cyanotic congenital cardiac malformation. Rare at birth, it is exceptionally rare for cases to survive over 5 years. Three cases of porlonged survival aged eleven nineteen and thirty-four years are reported. In the latter case, the abnormality was probably aquired. Prolonged survival is related to a collateral pulmonary circulation. Surgical treatment is discussed with respect to the anatomical features. Good results were obtained in the two operated cases.
室间隔完整的肺动脉瓣闭锁是一种罕见的发绀型先天性心脏畸形。出生时罕见，病例存活超过5年极为罕见。本文报告了3例存活时间较长的病例，年龄分别为11岁、19岁和34岁。在后一例中，这种异常可能是后天获得的。长期存活与肺侧支循环有关。根据解剖学特征讨论了手术治疗方法。在2例接受手术的病例中取得了良好的效果。
