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[先天性胆总管囊肿的产前诊断]

[Antenatal diagnosis of a choledocal cyst].

作者信息

Couto J C F, Leite J M B, Machado A V, Souza N S T, Silva M V R

机构信息

Service de Médecine Foetale, Santa Casa de Belo Horizonte (Hôtel Dieu), Av Francisco Sales 1111, Belo Horizonte, MG, Brésil.

出版信息

J Radiol. 2002 May;83(5):647-9.

PMID:12063428
Abstract

Choledocal cyst is a rare anomaly that usually becomes symptomatic during childhood. Forty to sixty percent of choledocal cysts are diagnosed before 10 years old, usually when complications occur. Today, because of advances in sonographic imaging, some cysts can de diagnosed before birth. The major prognostic factor is the development of complications such as hepatic fibrosis. Early treatment, after postnatal ultrasonography assessment, can reduce the incidence of serious complications. The authors report a case of a choledocal cyst diagnosed at 23 weeks gestation.

摘要

胆总管囊肿是一种罕见的异常情况,通常在儿童期出现症状。40%至60%的胆总管囊肿在10岁前被诊断出来,通常是在出现并发症时。如今,由于超声成像技术的进步,一些囊肿在出生前就能被诊断出来。主要的预后因素是诸如肝纤维化等并发症的发生。产后超声评估后尽早治疗可降低严重并发症的发生率。作者报告了一例在妊娠23周时被诊断出的胆总管囊肿病例。

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