伴有大量骨质溶解（戈勒姆综合征）的乳糜胸。

Chylothorax associated with massive osteolysis (Gorham's syndrome).

作者信息

Fujiu Koichi, Kanno Ryuzo, Suzuki Hiroyuki, Nakamura Naoya, Gotoh Mitsukazu

机构信息

First Department of Surgery, Fukushima Medical University, Japan.

出版信息

Ann Thorac Surg. 2002 Jun;73(6):1956-7. doi: 10.1016/s0003-4975(02)03413-6.

DOI:10.1016/s0003-4975(02)03413-6

PMID:12078801

Abstract

We report a 15-year-old boy with bilateral chylothorax complicating Gorham's syndrome. Thoracic duct ligation failed to prevent fluid reaccumulation. The patient died of lymphocytopenia. Autopsy revealed vascular proliferation in the parietal and visceral pleura as well as in the ribs, which seemed to cause persistent chylothorax responsible for the poor prognosis of this patient. We reviewed treatments provided to 22 patients reported in the literature with Gorham's syndrome and chylothorax.

摘要

我们报告一名15岁患戈勒姆综合征并发双侧乳糜胸的男孩。胸导管结扎未能阻止液体再次积聚。患者死于淋巴细胞减少症。尸检显示壁层和脏层胸膜以及肋骨中有血管增生，这似乎导致了持续性乳糜胸，造成该患者预后不良。我们回顾了文献中报道的22例患有戈勒姆综合征和乳糜胸的患者所接受的治疗。