[肠系膜和结肠系膜囊性淋巴管瘤。诊断与治疗管理]
[IMesenteric and mesocolic cystic lymphangiomas. Diagnostic and therapeutic management].
作者信息
Mabrut J Y, Grandjean J P, Henry L, Chappuis J P, Partensky C, Barth X, Tissot E
机构信息
Service de chirurgie générale, digestive et de transplantation hépatique, hôpital de la Croix-Rousse, 103, Grande-rue-de-la-Croix-Rousse, 69317 Lyon 04, France.
出版信息
Ann Chir. 2002 May;127(5):343-9. doi: 10.1016/s0003-3944(02)00770-8.
STUDY AIM
Study of clinical, diagnostic and therapeutic aspects of mesenteric and mesocolic cystic lymphangiomas.
MATERIAL AND METHODS
15 cases were retrospectively analysed: 5 adults (mean age 36.8 years, range 26 to 46) and 10 children (mean age 23 months, range 0 to 5 years). Diagnosis was prenatal in 1 case. Symptoms were: abdominal pain (80%), fever (20%), abdominal mass (46%), occlusive syndrome (33%), chylous ascitis 1 case. Tumours were mesenteric (86%) or mesocolic (13%).
RESULTS
Complete resection was performed in 11 cases (including 10 bowel resections), incomplete resections in 3 and doxycycline sclerotherapy once. Mean follow-up is 5 years. One recurrence occurred 6 years after complete resection and 1 tumour increased after incomplete resection. Patient treated by sclerotherapy was non symptomatic with a 3.5 years follow-up after last injection.
CONCLUSION
Mesenteric and mesocolic cystic lymphangiomas are congenital benign tumours. Complete resection should be performed whenever possible. Intracystic sclerotherapy with doxycyclin is possible for unresectable lymphangiomas.
研究目的
肠系膜和结肠系膜囊性淋巴管瘤的临床、诊断及治疗方面的研究。
材料与方法
对15例病例进行回顾性分析，其中5例为成人（平均年龄36.8岁，范围26至46岁），10例为儿童（平均年龄23个月，范围0至5岁）。1例产前诊断。症状包括：腹痛（80%）、发热（20%）、腹部肿块（46%）、梗阻综合征（33%）、乳糜性腹水1例。肿瘤位于肠系膜（86%）或结肠系膜（13%）。
结果
11例进行了完整切除（包括10例肠切除），3例为不完全切除，1例进行了强力霉素硬化治疗。平均随访5年。1例在完整切除6年后复发，1例在不完全切除后肿瘤增大。接受硬化治疗的患者在最后一次注射后随访3.5年无症状。
结论
肠系膜和结肠系膜囊性淋巴管瘤是先天性良性肿瘤。尽可能进行完整切除。对于无法切除的淋巴管瘤，可采用强力霉素进行囊内硬化治疗。
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