Mabrut J Y, Grandjean J P, Henry L, Chappuis J P, Partensky C, Barth X, Tissot E
Service de chirurgie générale, digestive et de transplantation hépatique, hôpital de la Croix-Rousse, 103, Grande-rue-de-la-Croix-Rousse, 69317 Lyon 04, France.
Ann Chir. 2002 May;127(5):343-9. doi: 10.1016/s0003-3944(02)00770-8.
Study of clinical, diagnostic and therapeutic aspects of mesenteric and mesocolic cystic lymphangiomas.
15 cases were retrospectively analysed: 5 adults (mean age 36.8 years, range 26 to 46) and 10 children (mean age 23 months, range 0 to 5 years). Diagnosis was prenatal in 1 case. Symptoms were: abdominal pain (80%), fever (20%), abdominal mass (46%), occlusive syndrome (33%), chylous ascitis 1 case. Tumours were mesenteric (86%) or mesocolic (13%).
Complete resection was performed in 11 cases (including 10 bowel resections), incomplete resections in 3 and doxycycline sclerotherapy once. Mean follow-up is 5 years. One recurrence occurred 6 years after complete resection and 1 tumour increased after incomplete resection. Patient treated by sclerotherapy was non symptomatic with a 3.5 years follow-up after last injection.
Mesenteric and mesocolic cystic lymphangiomas are congenital benign tumours. Complete resection should be performed whenever possible. Intracystic sclerotherapy with doxycyclin is possible for unresectable lymphangiomas.
肠系膜和结肠系膜囊性淋巴管瘤的临床、诊断及治疗方面的研究。
对15例病例进行回顾性分析,其中5例为成人(平均年龄36.8岁,范围26至46岁),10例为儿童(平均年龄23个月,范围0至5岁)。1例产前诊断。症状包括:腹痛(80%)、发热(20%)、腹部肿块(46%)、梗阻综合征(33%)、乳糜性腹水1例。肿瘤位于肠系膜(86%)或结肠系膜(13%)。
11例进行了完整切除(包括10例肠切除),3例为不完全切除,1例进行了强力霉素硬化治疗。平均随访5年。1例在完整切除6年后复发,1例在不完全切除后肿瘤增大。接受硬化治疗的患者在最后一次注射后随访3.5年无症状。
肠系膜和结肠系膜囊性淋巴管瘤是先天性良性肿瘤。尽可能进行完整切除。对于无法切除的淋巴管瘤,可采用强力霉素进行囊内硬化治疗。