Bajaj Mandeep S, Nainiwal Sanjeev K, Pushker Neelam, Sen Seema
Oculoplastic and Paediatric Ophthalmology Services, Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, India.
Orbit. 2002 Sep;21(3):205-8. doi: 10.1076/orbi.21.3.205.7175.
Neurofibroma is an extremely rare neural tumor of the lacrimal sac. We present a case of neurofibroma of the lacrimal sac in a 45-year-old lady. Based on the history of intermittent epiphora, presence of a mass in the lacrimal sac region, dacryocystogram suggestive of space occupying lesion within the lacrimal sac and computed tomographic image of a tumor lying in the lacrimal fossa region, a tentative diagnosis of lacrimal sac neoplasm was made. Excision of the tumor with repair of the lacrimal sac was performed. Histopathology proved it to be neurofibroma of the lacrimal sac. Until now, only four cases have been reported worldwide. The paucity of reported cases limits our knowledge regarding the natural course, treatment, results and prognosis of this tumor.
神经纤维瘤是一种极其罕见的泪囊神经肿瘤。我们报告一例45岁女性泪囊神经纤维瘤病例。根据间歇性溢泪病史、泪囊区肿块的存在、泪囊造影提示泪囊内占位性病变以及泪囊窝区域肿瘤的计算机断层扫描图像,初步诊断为泪囊肿瘤。进行了肿瘤切除及泪囊修复手术。组织病理学证实为泪囊神经纤维瘤。到目前为止,全球仅报道了4例。报告病例的稀缺限制了我们对该肿瘤自然病程、治疗、结果及预后的了解。