Wallerstein Robert, Oh Tracey, Durcan Judy, Abdelhak Yaakov, Clachko Mark, Aviv Hana
Genetics Service, Department of Pediatrics, Hackensack University Medical Center, Hackensack, NJ 07601, USA.
Prenat Diagn. 2002 Aug;22(8):722-4. doi: 10.1002/pd.391.
We report the prenatal diagnosis of trisomy 6 mosaicism via amniocentesis, in which trisomy 6 cells were identified in three of five culture vessels with 33% (5/15) of colonies showing trisomic cells. The pregnancy was electively terminated and examination revealed minor abnormalities (shortening of the femurs, micrognathia, posterior malrotation of the ears, and bilateral camptomelia of the second digit of the hands and fifth digits of the feet). Cytogenetic analysis of the placenta showed trisomy 6 in 100% of 20 cells studied. Karyotype was 46,XX in 100 cells examined from fetal skin. There are relatively few prenatally diagnosed cases of mosaic trisomy 6 at amniocentesis. Confined placental mosaicism (CPM) has been postulated in other cases where follow-up cytogenetic studies were not available. The present case differs from those previously reported, as it appears to represent CPM of chromosome 6 with phenotypic effects to the fetus.
我们报告了通过羊膜穿刺术进行的6号染色体三体嵌合体的产前诊断,在五个培养皿中的三个中鉴定出6号染色体三体细胞,33%(5/15)的集落显示为三体细胞。该妊娠被选择性终止,检查发现有轻微异常(股骨缩短、小颌畸形、耳后旋、双手第二指和双足第五指双侧先天性弯曲)。对胎盘的细胞遗传学分析显示,在所研究的20个细胞中,100%为6号染色体三体。从胎儿皮肤检查的100个细胞中,核型为46,XX。在羊膜穿刺术中,产前诊断为6号染色体三体嵌合体的病例相对较少。在其他无法进行后续细胞遗传学研究的病例中,推测存在局限型胎盘嵌合体(CPM)。本病例与先前报道的病例不同,因为它似乎代表了6号染色体的CPM,并对胎儿产生了表型影响。