Minegishi Kazunori, Kusaka Yasuko, Shirane Reizo, Yoshimoto Takashi
Department of Neurosurgery, Graduate School of Medicine, Tohoku University, 1-1 Seiryo-cho, Aoba-ku, Sendai-city, Miyagi 980-8574, Japan.
No Shinkei Geka. 2002 Sep;30(9):967-71.
The authors present a case of congenital dermal sinus tract with epidermoid tumor. This 1-year-old boy was referred to the pediatric service of another hospital with recurrent pyrexia of unknown origin in April, 1999. The pediatrician found two dimples, pigmentation, and coarse hairs on the midline in his sacral region. Computerized tomography (CT) scans revealed a spina bifida below the S1 level. Magnetic resonance (MR) imaging revealed a dermal sinus tract in the cranial direction to a cystic tumor at L2-4 levels. He was transferred to our hospital, and the tract and tumor were totally removed in June, 1999. The histological findings and Escherichia coli in the smear culture of the tumor contents identified it as an infected congenital dermal sinus tract with epidermoid tumor. The patient received antibiotics for two weeks after surgery and there was no clinical or radiographic recurrence of either infection or tumor. The authors propose early diagnosis and radical treatment, because infected congenital dermal sinus tract often leads to a bad neurological prognosis.
作者报告了一例伴有表皮样瘤的先天性真皮窦道病例。该1岁男孩于1999年4月因不明原因反复发热被转诊至另一家医院的儿科。儿科医生在其骶部中线发现两个酒窝、色素沉着和粗糙毛发。计算机断层扫描(CT)显示S1水平以下脊柱裂。磁共振(MR)成像显示一条真皮窦道向头侧延伸至L2 - 4水平的囊性肿瘤。他被转至我院,并于1999年6月将窦道和肿瘤完全切除。肿瘤内容物涂片培养的组织学检查结果及大肠杆菌表明其为伴有表皮样瘤的感染性先天性真皮窦道。患者术后接受了两周抗生素治疗,感染或肿瘤均无临床或影像学复发。作者建议早期诊断和根治性治疗,因为感染性先天性真皮窦道常导致不良的神经学预后。