Corberand J, Pris J, Dutau G, Rumeau J L, Regnier C
Arch Fr Pediatr. 1975 Mar;32(3):275-863.
A Fanconi's disease was discovered in a 9 1/2 year old girl. She received androgens daily and died with a severe aplastic attack after 4 years of evolution. Hepatic involvement of treatment with androgens was regularly checked. Autopsy however, showed a multinodular adenoma of the liver without any malignant manifestation. Relationships between aplastic anemia, long-term treatment with androgens and tumour of the liver are discussed. The difficulty of in vivo diagnosis is emphasized.
在一名9岁半的女孩身上发现了范科尼氏病。她每天接受雄激素治疗,病程4年后死于严重的再生障碍发作。对雄激素治疗的肝脏受累情况进行了定期检查。然而,尸检显示肝脏有多发性结节性腺瘤,无任何恶性表现。讨论了再生障碍性贫血、长期雄激素治疗与肝脏肿瘤之间的关系。强调了体内诊断的困难。