Cystine depletion of cystinotic cells by aminothiols.
作者信息
Thoene J G, Oshima R G, Crawhall J C, Schneider J A
机构信息
Department of Pediatrics, University of California, San Diego.
出版信息
Proc R Soc Med. 1977;70 Suppl 3(Suppl 3):37-40. doi: 10.1177/00359157770700S314.
Abstract
摘要
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A Personal History of Cystinosis by Dr. Jerry Schneider.《胱氨酸病个人史》，作者杰里·施耐德博士。
Cells. 2022 Mar 10;11(6):945. doi: 10.3390/cells11060945.
本文引用的文献
1
Increased free-cystine content of fibroblasts cultured from patients with cystinosis.胱氨酸病患者培养的成纤维细胞中游离胱氨酸含量增加。
Biochem Biophys Res Commun. 1967 Nov 30;29(4):527-31. doi: 10.1016/0006-291x(67)90516-5.
2
Effect of penicillamine on cystinuria.青霉胺对胱氨酸尿症的影响。
Br Med J. 1963 Mar 2;1(5330):588-90. doi: 10.1136/bmj.1.5330.588.
3
Use of dimercaprol or pencillamine in the treatment of cystinosis.使用二巯丙醇或青霉胺治疗胱氨酸病。
Lancet. 1961 Oct 21;2(7208):909-10.
4
Increased cystine in leukocytes from individuals homozygous and heterozygous for cystinosis.胱氨酸病纯合子和杂合子个体白细胞中胱氨酸增加。
Science. 1967 Sep 15;157(3794):1321-2. doi: 10.1126/science.157.3794.1321.
5
Penicillamine treatment of cystinosis.青霉胺治疗胱氨酸病。
Acta Paediatr Scand. 1967 May;56(3):243-8. doi: 10.1111/j.1651-2227.1967.tb15374.x.
6
Cystinosis. Plasma cystine and cysteine concentrations and the effect of D-penicillamine and dietary treatment.胱氨酸病。血浆胱氨酸和半胱氨酸浓度以及青霉胺和饮食治疗的效果。
Am J Med. 1968 Mar;44(3):330-9. doi: 10.1016/0002-9343(68)90104-6.
7
Cystinosis: therapeutic implications of in vitro studies of cultured fibroblasts.胱氨酸病：培养成纤维细胞体外研究的治疗意义
J Pediatr. 1971 May;78(5):833-6. doi: 10.1016/s0022-3476(71)80355-4.
8
Decrease in free cystine content of cultured cystinotic fibroblasts by ascorbic acid.抗坏血酸降低培养的胱氨酸病成纤维细胞的游离胱氨酸含量。
Science. 1974 Dec 13;186(4168):1040-2. doi: 10.1126/science.186.4168.1040.
9
10
Use of dithiothreitol to correct cystine storage in cultured cystinotic fibroblasts.使用二硫苏糖醇纠正培养的胱氨酸病成纤维细胞中的胱氨酸储存。
Lancet. 1970 Apr 18;1(7651):811-2. doi: 10.1016/s0140-6736(70)92411-6.
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