Ben Abdallah Néjib, Cherif Lotfi, Khiari Karima, Hadj Ali Insaf, Turki Sami, Mezni Faouzi, Ben Jilani Sarrah, Ben Maïz Hédi
Service de Médecine Interne A, Hôpital Charles Nicolle, 1006 Tunis, Tunisie.
Tunis Med. 2002 Mar;80(3):158-61.
Suprasellar germinomas are frequent in childhood and adolescence, particularly in male sex. The clinical and neuroendocrine abnormalities depend of tumor localization: Increased intracranial pressure, visual disturbances, hypopituitarism, Parinaud syndrome. We report two cases of suprasellar germinoma in young male patients (16 and 18 years old). The first patient hrad corticotorpin insufficiency and clinical signs of hypothyroïdism and hypogonadism. The second had central hypocorticism, hypothyroïdism and hypogonadism associated with central diabetes insipidus and hyperprolactinemia. The diagnosis of germinoma was confirmed after surgery by anatomopathologic examination in the first case and by stereotaxic biopsy in the second case. Treatment by radiotherapy improves prognosis of this disease.
鞍上生殖细胞瘤在儿童和青少年中较为常见,尤其是男性。临床和神经内分泌异常取决于肿瘤的位置:颅内压升高、视觉障碍、垂体功能减退、帕里诺德综合征。我们报告了两例年轻男性患者(16岁和18岁)的鞍上生殖细胞瘤病例。首例患者有促肾上腺皮质激素不足以及甲状腺功能减退和性腺功能减退的临床症状。第二例患者有中枢性肾上腺皮质功能减退、甲状腺功能减退和性腺功能减退,并伴有中枢性尿崩症和高催乳素血症。首例患者术后经病理检查确诊为生殖细胞瘤,第二例患者经立体定向活检确诊。放射治疗可改善该病的预后。