Konovalov A N, Pitskhelauri D I, Arutiounov N V
Burdenko Neurosurgery Institute, Moscow, Russia.
Acta Neurochir (Wien). 2002 Sep;144(9):909-15; discussion 915. doi: 10.1007/s00701-002-0976-8.
Vein of Galen aneurysm is a rare congenital anomaly of cerebral circulation and occurs mainly in newborns and children. The spontaneously thrombosed vein of Galen aneurysm is especially rare and an uncommonly reported event.
Two patients with a spontaneously thrombosed vein of Galen aneurysm were operated on at our institute. CT and MRI demonstrated space-occupying lesions of the pineal region and two other masses in the posterior fossa in the second case. The first described case should be referred to as the true type of aneurysm. The vascular malformation, revealed in the second case should be referred to as the false type. In this case the vein of Galen was enlarged to a gigantic size due to the blood drainage from the arteriovenous malformation supplying it from the inferior posterior cerebellar artery.
Thrombosed aneurysmal sacs were resected totally by subtentorial supracerebellar and median suboccipital approaches.
The authors report two cases of successful surgical resection of a thrombosed vein of Galen aneurysm in children. Diagnostic features are considered and the informative value of magnetic resonance imaging is stressed. The principles of choosing the right approach and dissection techniques of thrombosed aneurysms of the vein of Galen are described.
大脑大静脉动脉瘤是一种罕见的先天性脑循环异常,主要发生于新生儿和儿童。自发性血栓形成的大脑大静脉动脉瘤尤为罕见,且报道较少。
我院对2例自发性血栓形成的大脑大静脉动脉瘤患者进行了手术。CT和MRI显示松果体区占位性病变,第二例患者后颅窝还有另外两个肿块。首例报道的病例应称为真性动脉瘤类型。第二例显示的血管畸形应称为假性类型。在该病例中,由于小脑后下动脉供血的动静脉畸形导致血液引流,大脑大静脉扩大至巨大尺寸。
采用枕下小脑上和枕下正中入路完全切除血栓形成的动脉瘤囊。
作者报告了2例成功手术切除儿童血栓形成的大脑大静脉动脉瘤的病例。考虑了诊断特征并强调了磁共振成像的信息价值。描述了选择正确入路的原则以及大脑大静脉血栓形成动脉瘤的解剖技术。