Goyal Anju, Babu S Nagesh, Kim Vaiphei, Katariya S, Rao K L N
Department of Pediatric Surgery, Pathology, and Radiodiagnosis, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
J Pediatr Surg. 2002 Oct;37(10):E29. doi: 10.1053/jpsu.2002.35440.
The case of a 9-year-old boy with hemangioendothelioma of the liver and spleen who presented with consumptive coagulopathy one month after sustaining a blunt trauma to his abdomen is reported. A contrast enhanced computed tomography scan of the abdomen showed a ruptured spleen with multiple lesions in the liver that were enhancing with contrast. On exploration, the child was found to have splenic rupture with multiple vascular lesions of the liver. A splenectomy with liver biopsy was done. The histopathologic examination found that both the liver and spleen had a similar tumor morphology characteristic of an epithelioid and spindle cell hemangioendothelioma. The child ultimately died of relentless consumptive coagulopathy.
报告了一名9岁男孩的病例,该男孩患有肝脾血管内皮瘤,在腹部遭受钝性创伤1个月后出现消耗性凝血病。腹部增强计算机断层扫描显示脾脏破裂,肝脏有多个病变,造影剂增强。术中发现患儿脾脏破裂,肝脏有多个血管病变。进行了脾切除术和肝脏活检。组织病理学检查发现肝脏和脾脏具有相似的肿瘤形态特征,为上皮样和梭形细胞血管内皮瘤。该患儿最终死于难以控制的消耗性凝血病。