Girot R, Vedrenne J
Arch Fr Pediatr. 1975 Nov;32(9):871-8.
A 9 year old boy presented an "idiopathic" retroperitoneal fibrosis. Fibrosis extended to the liver, compressing the major biliary tree, the portal vein, the urinary tract and the inferior vena cava. The process led two successive bilio-digestive shunts and was controlled after one year corticosteroid treatment. A malignant lymphoma was responsible for the death which occurred 4 years after the initial symptoms of retroperitoneal fibrosis.
一名9岁男孩患有“特发性”腹膜后纤维化。纤维化蔓延至肝脏,压迫主要胆管、门静脉、泌尿道和下腔静脉。该病情导致了两次连续的胆肠分流术,并在接受一年的皮质类固醇治疗后得到控制。恶性淋巴瘤导致了在腹膜后纤维化初始症状出现4年后的死亡。