Complete correction of double-outlet right ventricle with situs inversus, 1-loop, and 1-malposition (I,L,L) with subaortic VSD and pulmonary stenosis.

The repair a unique case of double-outlet right ventricle is reported. This case illustrates the increasingly difficult problem of developing an appropriate nomenclature in complex congenital heart disease. A classification of double-outlet right ventricle based upon Van Praagh's symbolic terminology is suggested.