Crabbe D C G
Department of Paediatric Surgery, Clarendon Wing, Leeds General Infirmary, Leeds LS2 9NS, UK.
Paediatr Respir Rev. 2003 Mar;4(1):74-8.
Congenital isolated tracheo-oesophageal fistula is a rare malformation that presents with a characteristic triad of symptoms: choking and cyanosis on feeding, recurrent lower respiratory tract infection and abdominal distension. Children are invariably symptomatic from birth, although the symptoms may be intermittent and may vary in severity. A high index of suspicion is required because the symptoms are not specific. Establishing the diagnosis can be difficult and neither radiology nor bronchoscopy is infallible. Surgical division of the fistula is curative.
先天性孤立性气管食管瘘是一种罕见的畸形，其特征性症状三联征为：进食时呛咳和发绀、反复下呼吸道感染及腹胀。患儿出生时往往就有症状，尽管症状可能是间歇性的，严重程度也可能不同。由于症状不具特异性，因此需要高度怀疑。确诊可能很困难，放射学检查和支气管镜检查都并非万无一失。手术切断瘘管可治愈该病。
