Minor Lloyd B, Carey John P, Cremer Phillip D, Lustig Lawrence R, Streubel Sven-Olrik, Ruckenstein Michael J
Department of Otolaryngology-Head and Neck Surgery, The Johns Hopkins University School of Medicine, Baltimore, Maryland, USA.
Otol Neurotol. 2003 Mar;24(2):270-8. doi: 10.1097/00129492-200303000-00023.
To identify patients with superior semicircular canal dehiscence and apparent conductive hearing loss and to define the cause of the air-bone gap.
Prospective study of patients with superior canal dehiscence. SETTING Tertiary referral center.
Vestibular and/or auditory findings indicative of canal dehiscence and demonstration of superior canal dehiscence on computed tomography of the temporal bone.
Vestibular-evoked myogenic potentials, three-dimensional eye movement recordings, and surgical resurfacing of the superior canal.
Association of superior canal dehiscence with an air-bone gap on audiometry.
Four patients with dehiscence of bone overlying the superior canal were found to have air-bone gaps in the affected ears that were greatest at lower frequencies and averaged 24 +/- 7 dB over the frequency range of 250 to 4,000 Hz. Three of these patients had undergone stapedectomy before the identification of superior canal dehiscence. The air-bone gap was unchanged postoperatively. Each patient had an intact vestibular-evoked myogenic potential (VEMP) response from the affected ear, a finding that would not have been expected based on a middle ear cause of conductive hearing loss. One patient underwent resurfacing of the superior canal through a middle fossa approach. Postoperatively, his vestibular symptoms were relieved, and his air conduction thresholds were improved by 20 dB.
Superior canal dehiscence can result in apparent conductive hearing loss. The third mobile window created by the dehiscent superior canal results in dissipation of acoustic energy and is a cause of inner ear conductive hearing loss.
识别患有上半规管裂和明显传导性听力损失的患者,并确定气骨导差的原因。
对上半规管裂患者进行前瞻性研究。研究地点为三级转诊中心。
前庭和/或听觉检查结果提示存在半规管裂,且颞骨计算机断层扫描显示上半规管裂。
前庭诱发肌源性电位、三维眼动记录,以及对上半规管进行手术修复。
上半规管裂与听力测定中气骨导差的相关性。
发现4例上半规管上方骨质裂开的患者,患耳存在气骨导差,在低频时最为明显,在250至4000Hz频率范围内平均为24±7dB。其中3例患者在确诊上半规管裂之前已接受了镫骨切除术。术后气骨导差未改变。每位患者患耳的前庭诱发肌源性电位(VEMP)反应均正常,基于传导性听力损失的中耳病因,这一结果并不预期。1例患者通过中颅窝入路对上半规管进行了修复。术后,他的前庭症状得到缓解,气导阈值提高了20dB。
上半规管裂可导致明显的传导性听力损失。裂开的上半规管形成的第三个活动窗导致声能消散,是内耳传导性听力损失的一个原因。