Pouliadia G P, Wellauer J, Wirth W
Lymphology. 1976 Mar;9(1):28-35.
A case of diffuse lymphangiomyomatosis with involvement of the large veins of the body is reported. The clinical, pathologoanatomic and especially the roentgenologic findings are described. Interstitial lung thickening, pleural effusions and spontaneous pneumothorax are findings which together with a stasis in the lymphatic system strongly suggest the diagnosis. The extensive involvement of the venous system supports the theory of a hamartomatous nature of the disease.
报告了一例累及身体大静脉的弥漫性淋巴管肌瘤病病例。描述了其临床、病理解剖学,尤其是放射学检查结果。间质性肺增厚、胸腔积液和自发性气胸等表现,连同淋巴系统的淤滞,强烈提示了诊断。静脉系统的广泛受累支持了该病错构瘤性质的理论。