Rabin Doron, Ang Lee Cyn, Megyesi Joseph, Lee Donald H, Duggal Neil
Department of Clinical Neurological Sciences, Division of Neurosurgery, London Health Sciences Centre, University of Western Ontario, London, Ontario, Canada.
Neurosurgery. 2003 Apr;52(4):950-4; discussion 954. doi: 10.1227/01.neu.0000053025.36216.3c.
Desmoplastic fibroma is a benign bone tumor that can be locally aggressive. It usually occurs in the long bones and mandible. We report on a patient with a desmoplastic fibroma arising in the temporal bone and review previously published cases of desmoplastic fibroma originating within the cranium.
A 43-year-old woman presented with a 12-year history of progressively worsening head asymmetry. Magnetic resonance imaging and computed tomography demonstrated a mass originating from the bone and involving the adjacent soft tissues.
A temporal parietal craniectomy was performed with excision of a large tumor involving the bone. An acrylic cranioplasty was used to replace the bone. Pathological examination of the lesion identified desmoplastic fibroma of the cranium. After surgery, the patient's cranial asymmetry was corrected.
Desmoplastic fibroma of the cranium is rare. Surgical resection is the treatment of choice.
促结缔组织增生性纤维瘤是一种具有局部侵袭性的良性骨肿瘤。它通常发生于长骨和下颌骨。我们报告一例发生于颞骨的促结缔组织增生性纤维瘤患者，并回顾先前发表的起源于颅骨内的促结缔组织增生性纤维瘤病例。
一名43岁女性，有12年逐渐加重的头部不对称病史。磁共振成像和计算机断层扫描显示有一源于骨质并累及相邻软组织的肿块。
行颞顶部颅骨切除术，切除累及骨质的大肿瘤。使用丙烯酸颅骨成形术修复颅骨。病变的病理检查确诊为颅骨促结缔组织增生性纤维瘤。术后，患者的颅骨不对称得以纠正。
颅骨促结缔组织增生性纤维瘤罕见。手术切除是首选治疗方法。
