Bahri I, Kallel R, Gouiaa N, Boudawara Z, Boudawara T S
Laboratoire d'anatomie et de cytologie pathologiques, CHU Habib Bourguiba, route El Aïn Km 0.5, 3029 Sfax, Tunisia.
Neurochirurgie. 2011 Feb;57(1):39-41. doi: 10.1016/j.neuchi.2010.07.003. Epub 2010 Sep 28.
Desmoplastic fibromas are uncommon osseous tumors that seldom involve the skull. These tumors are histologically benign but locally aggressive with a propensity for recurrence if resection is partial. To our knowledge, only 16 cases have been reported in the literature, seven of which concerned children. We report a further case of a desmoplastic fibroma of the skull in a 3-year-old boy who presented with a right parietal mass. The CT scan showed a lytic mass with brain compression and cortical destruction. The patient underwent a craniectomy and complete mass resection. Histological diagnosis was desmoplastic fibroma. Postoperative progress was normal without recurrence 6 months later.
促纤维增生性纤维瘤是一种罕见的骨肿瘤，很少累及颅骨。这些肿瘤在组织学上是良性的，但具有局部侵袭性，如果手术切除不彻底则容易复发。据我们所知，文献中仅报道了16例，其中7例为儿童患者。我们报告了1例3岁男孩颅骨促纤维增生性纤维瘤的病例，该患儿表现为右顶叶肿块。CT扫描显示一个溶骨性肿块，伴有脑受压和皮质破坏。患者接受了颅骨切除术和肿块全切术。组织学诊断为促纤维增生性纤维瘤。术后恢复正常，6个月后无复发。
