Widdess-Walsh Peter, Friedman Neil Roy
Department of Neurology, Cleveland Clinic Foundation, Ohio 44195, USA.
J Child Neurol. 2003 Apr;18(4):304-5. doi: 10.1177/08830738030180040301.
Sturge-Weber syndrome is characterized by a facial vascular nevus associated with an ipsilateral leptomeningeal angioma. Variants of this classical presentation have been described in the literature, some of which have prognostic significance. We report a magnetic resonance imaging (MRI)-confirmed variant of a leptomeningeal angioma contralateral to the facial nevus. We describe one patient with Sturge-Weber syndrome who presented with a left-sided facial nevus, left eye glaucoma, episodes of left-sided weakness, and right-sided leptomeningeal angiomatosis by gadolinium-enhanced brain MRI. The literature regarding variants of Sturge-Weber syndrome and their prognosis is reviewed. The prognosis for this variant is likely similar to Sturge-Weber syndrome with an ipsilateral leptomeningeal angioma.
斯特奇-韦伯综合征的特征是面部血管痣伴同侧软脑膜血管瘤。文献中已描述了这种经典表现的变体，其中一些具有预后意义。我们报告了一例经磁共振成像（MRI）证实的与面部痣对侧的软脑膜血管瘤变体。我们描述了一名患有斯特奇-韦伯综合征的患者，其表现为左侧面部痣、左眼青光眼、左侧无力发作，经钆增强脑MRI显示右侧软脑膜血管瘤病。本文对斯特奇-韦伯综合征变体及其预后的相关文献进行了综述。这种变体的预后可能与伴有同侧软脑膜血管瘤的斯特奇-韦伯综合征相似。
