El Bahri-Ben Mrad F, Zaouachi N, Fredj M, Ben Mrad S, Mrabet A
Service de Neurologie, EPS Charles Nicolle, Tunis, Tunisie.
Rev Neurol (Paris). 2003 May;159(5 Pt 1):574-6.
Extramedullary hematopoiesis is an unusual cause of spinal cord compression. We report the case of a 39-year-old man who presented symptoms of progressive dorsal spinal cord compression. Hemogramm showed erythrocytosis with microcytosis. Hemoglobin electrophoresis revealed heterozygous beta-thalassemia. Diagnosis of extramedullary hematopoiesis was based on magnetic resonance imaging findings. Radiological and therapeutic options in this rare condition are briefly discussed.
髓外造血是脊髓压迫症的一种罕见病因。我们报告一例39岁男性患者,其出现进行性脊髓背侧压迫症状。血常规显示红细胞增多伴小红细胞症。血红蛋白电泳显示杂合子β地中海贫血。髓外造血的诊断基于磁共振成像结果。本文简要讨论了这种罕见病症的影像学及治疗选择。