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范德伍德综合征下唇修复术

Lower lip repair in Van der Woude syndrome.

作者信息

Capon-Degardin N, Martinot-Duquennoy V, Auvray G, Pellerin P

机构信息

Plastic and Reconstructive Surgery Department, University Hospital, Lille, France.

出版信息

Eur J Pediatr Surg. 2003 Apr;13(2):92-6. doi: 10.1055/s-2003-39584.

Abstract

Van der Woude syndrome is an unusual congenital malformation. It combines lower lip sinuses with a cleft lip and/or palate. The asymmetry appears more pronounced due to lower lip hypotonia and procheilia, which are more unaesthetic than the fistulae themselves. The malformation of the orbicularis oris muscle in its medial part induces the hypotonic aspect of the lower lip, which contrasts with the retracted scarred upper lip after the cleft has been repaired. It is also responsible for a real bilabial asymmetry. For many years, the most common surgical treatment was simple excision of the sinuses. Bad functional repair results prompted the authors to try another surgical procedure, the split-lip advancement technique as described by Mutaf. The authors report here on 8 operated children out of 25 patients followed up for Van der Woude syndrome. They evaluated the results according to the appearance of the lip when relaxed, its functional aspect, and the satisfaction of the parents or the child. Our results point to the importance of early surgical treatment, radical excision of dysplastic tissue and the repair of lip muscles to restore good lip functionality and satisfactory bilabial symmetry. The technique now used in our department has made it possible for us to achieve these goals.

摘要

范德伍德综合征是一种罕见的先天性畸形。它表现为下唇窦道合并唇裂和/或腭裂。由于下唇张力减退和下唇前突,不对称显得更为明显,而下唇前突比窦道本身更不美观。口轮匝肌内侧部分的畸形导致下唇出现张力减退的外观,这与唇裂修复后上唇回缩且留有瘢痕形成了对比。它还导致了真正的双侧唇部不对称。多年来,最常见的手术治疗方法是单纯切除窦道。不良的功能修复结果促使作者尝试另一种手术方法,即穆塔夫描述的唇裂推进技术。作者在此报告了25例接受随访的范德伍德综合征患者中有8例接受了手术。他们根据唇部放松时的外观、功能状况以及家长或患儿的满意度来评估结果。我们的结果表明早期手术治疗、彻底切除发育异常组织以及修复唇部肌肉对于恢复良好的唇部功能和令人满意的双侧唇部对称的重要性。我们科室目前使用的技术使我们能够实现这些目标。

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