Thumkeo Dean, Keel Jeongsin, Ishizaki Toshimasa, Hirose Masaya, Nonomura Kimiko, Oshima Hiroko, Oshima Masanobu, Taketo Makoto M, Narumiya Shuh
Department of Pharmacology, Kyoto University Faculty of Medicine, Sakyo-ku, Kyoto 606-8501, Japan.
Mol Cell Biol. 2003 Jul;23(14):5043-55. doi: 10.1128/MCB.23.14.5043-5055.2003.
Rho-associated kinase (ROCK), including the ROCK-I and ROCK-II isoforms, is a protein kinase involved in signaling from Rho to actin cytoskeleton. However, in vivo functions of each ROCK isoform remain largely unknown. We generated mice deficient in ROCK-II by gene targeting. ROCK-II(-/-) embryos were found at the expected Mendelian frequency until 13.5 days postcoitum, but approximately 90% died thereafter in utero. ROCK-II(-/-) mice of both genders that survived were born runts, subsequently developed without gross abnormality, and were fertile. Whole-mount staining for a knocked-in lacZ reporter gene revealed that ROCK-II was highly expressed in the labyrinth layer of the placenta. Disruption of architecture and extensive thrombus formation were found in the labyrinth layer of ROCK-II(-/-) mice. While no obvious alteration in actin filament structures was found in the labyrinth layer of ROCK-II(-/-) placenta and stress fibers were formed in cultured ROCK-II(-/-) trophoblasts, elevated expression of plasminogen activator inhibitor 1 was found in ROCK-II(-/-) placenta. These results suggest that ROCK-II is essential in inhibiting blood coagulation and maintaining blood flow in the endothelium-free labyrinth layer and that loss of ROCK-II leads to thrombus formation, placental dysfunction, intrauterine growth retardation, and fetal death.
Rho相关激酶(ROCK),包括ROCK-I和ROCK-II亚型,是一种参与从Rho到肌动蛋白细胞骨架信号传导的蛋白激酶。然而,每种ROCK亚型在体内的功能仍 largely unknown。我们通过基因靶向产生了ROCK-II缺陷小鼠。在预期的孟德尔频率下,直到妊娠13.5天仍能发现ROCK-II(-/-)胚胎,但此后约90%在子宫内死亡。存活的雌雄ROCK-II(-/-)小鼠出生时体型矮小,随后发育无明显异常,且具有生育能力。对敲入的lacZ报告基因进行全胚胎染色显示,ROCK-II在胎盘的迷路层中高度表达。在ROCK-II(-/-)小鼠的迷路层中发现了结构破坏和广泛的血栓形成。虽然在ROCK-II(-/-)胎盘的迷路层中未发现肌动蛋白丝结构有明显改变,且在培养的ROCK-II(-/-)滋养层细胞中形成了应力纤维,但在ROCK-II(-/-)胎盘中发现纤溶酶原激活物抑制剂1的表达升高。这些结果表明,ROCK-II对于抑制无内皮迷路层中的血液凝固和维持血流至关重要,并且ROCK-II的缺失会导致血栓形成、胎盘功能障碍、宫内生长迟缓以及胎儿死亡。