Khoury Haytham, Lestou Valia S, Gascoyne Randy D, Bruyere Helene, Li Charles H, Nantel Stephen H, Dalal Bakul I, Naiman Shelly C, Horsman Douglas E
Leukemia/BMT Program of British Columbia, Vancouver, British Columbia, Canada.
Mod Pathol. 2003 Jul;16(7):716-24. doi: 10.1097/01.MP.0000077515.68734.85.
Intravascular lymphoma (IVL) is a rare neoplastic disease characterized by the presence of large malignant lymphoid cells in small vessels. It is often diagnosed at autopsy. Clinical manifestations are typically neurologic and dermatologic. Karyotypic abnormalities have been described in a small number of cases and have revealed complex alterations in the majority of cases. We have identified three cases of IVL with varied clinicopathological findings. Karyotypic analysis was undertaken by standard G-banding and supplemented by multi-colored karyotyping (M-FISH) to decipher the chromosomal content of marker chromosomes and undefined additions. M-FISH clarified the chromosomal abnormalities in two cases and unveiled cryptic translocations der(10)t(10;22), der(17)t(17;22), and balanced t(11;14). Comparison with previously published karyotypes revealed prominent involvement of chromosomes 1, 3, 6, 11, 14, and 18, similar to the pattern of clonal evolution in other B-cell lymphomas. The most frequent alterations seen were -6 or 6q- and +18 or dup(18q), with a minimally deleted region located at 6q21-q23 and a commonly amplified region located at 18q13-q23, respectively. Few differences between the classical and Asian variant of this disease were apparent at the karyotypic level. Cytogenetic analysis of additional cases supplemented by multicolor karyotyping may help identify the full spectrum of genetic alterations associated with IVL and assist in the delineation of the critical mutations associated with initiation and progression of this disease.
血管内淋巴瘤(IVL)是一种罕见的肿瘤性疾病,其特征是小血管内存在大的恶性淋巴细胞。该病常于尸检时被诊断出来。临床表现通常为神经和皮肤方面的症状。少数病例中描述了核型异常,且大多数病例显示出复杂的改变。我们鉴定出3例具有不同临床病理表现的IVL病例。通过标准G显带进行核型分析,并辅以多色核型分析(M-FISH),以解读标记染色体和未明确附加物的染色体组成。M-FISH明确了2例病例中的染色体异常,并揭示了隐匿性易位der(10)t(10;22)、der(17)t(17;22)和平衡易位t(11;14)。与先前发表的核型进行比较发现,1、3、6、11、14和18号染色体有显著受累,这与其他B细胞淋巴瘤的克隆进化模式相似。最常见的改变是-6或6q-以及+18或dup(18q),最小缺失区域分别位于6q21-q23,常见扩增区域位于18q13-q23。在核型水平上,该病的经典型和亚洲型之间几乎没有明显差异。通过多色核型分析补充的更多病例的细胞遗传学分析,可能有助于识别与IVL相关的全部遗传改变谱,并有助于描绘与该疾病的发生和进展相关的关键突变。