抗Jo-1阴性无肌病性皮肌炎中的致命性间质性肺纤维化
Fatal interstitial pulmonary fibrosis in anti-Jo-1-negative amyopathic dermatomyositis.
作者信息
High Whitney A, Cohen Jack B, Murphy Bettina A, Costner Melissa I
机构信息
Department of Dermatology, University of Texas Sothwestern Medical Center, Dallas, Texas 75390-9190, USA.
出版信息
J Am Acad Dermatol. 2003 Aug;49(2):295-8. doi: 10.1067/s0190-9622(03)01482-8.
Abstract
Amyopathic dermatomyositis (DM) describes a subpopulation with the cutaneous eruption of DM, but without muscle involvement. Interstitial pulmonary fibrosis is a recognized complication of DM, often correlated with antisynthetase enzymes, such as anti-Jo-1. We describe a case of fatal IPF in a patient with anti-Jo-1 antibody-negative amyopathic DM.
摘要
无肌病性皮肌炎（DM）是指具有皮肌炎皮肤表现但无肌肉受累的亚群。间质性肺纤维化是DM公认的并发症，常与抗合成酶抗体如抗Jo-1相关。我们报告1例抗Jo-1抗体阴性的无肌病性DM患者发生致命性特发性肺纤维化（IPF）的病例。
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