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伪装成右心室发育不良的心脏结节病。

Cardiac sarcoidosis masquerading as right ventricular dysplasia.

作者信息

Ott Peter, Marcus Frank I, Sobonya Richard E, Morady Fred, Knight Bradley P, Fuenzalida Charles E

机构信息

University of Arizona Health Sciences Center, Tucson, Arizona 85724, USA.

出版信息

Pacing Clin Electrophysiol. 2003 Jul;26(7 Pt 1):1498-503. doi: 10.1046/j.1460-9592.2003.t01-1-00217.x.

Abstract

Patients with cardiac sarcoidosis may present with clinical and morphological features similar to arrhythmogenic right ventricular dysplasia (ARVD) or cardiomyopathy (ARVC). Three cases of cardiac sarcoidosis are presented that clinically mimicked ARVD or ARVC until a pathology diagnosis of sarcoidosis was made at biopsy or autopsy. A diagnostic distinction, while often difficult to make, is important since treatment with corticosteroids may benefit those with sarcoidosis but is not expected to be useful in cases with ARVD or ARVC.

摘要

心脏结节病患者可能表现出与致心律失常性右心室发育不良(ARVD)或心肌病(ARVC)相似的临床和形态学特征。本文介绍了3例心脏结节病病例,这些病例在临床上与ARVD或ARVC相似,直到活检或尸检做出结节病的病理诊断。尽管通常很难做出诊断区分,但这很重要,因为使用皮质类固醇治疗可能对结节病患者有益,但对ARVD或ARVC患者预计无效。

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