Sroubková R, Meisnerová E, Vítková I
Gastroenterologické centrum IV. interní kliniky 1. LF UK a VFN, Praha.
Cas Lek Cesk. 2003;142(5):300-2.
Casuistry of a 59-year-old woman is presented. The patient was examined for nephrotic syndrome with relapsing stenosis of vena cava inferior treated with stent implantation and with severe protein-caloric malnutrition. She had macroglosy, mild hepatomegaly, severe impairment of gastrointestinal motility, and had in her history an operation of carpal tunnel. It took two years to establish the diagnosis, which was amyloidosis of AL.
介绍了一名59岁女性的病例情况。该患者因肾病综合征接受检查,伴有下腔静脉复发性狭窄并接受了支架植入治疗,同时患有严重的蛋白质 - 热量营养不良。她有巨舌症、轻度肝肿大、严重的胃肠动力障碍,且有腕管手术史。确诊花了两年时间,诊断结果为AL型淀粉样变性。