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严重遗传性因子VII缺乏症所致月经过多。病例1。

Menorrhagia caused by severe hereditary factor VII deficiency. Case 1.

作者信息

Aegerter Ch, Friess D, Alberio L

机构信息

Central Haematology Laboratory, Inselspital, University Hospital, 3010 Bern, Switzerland.

出版信息

Hamostaseologie. 2003 Aug;23(3):99-102.

PMID:12923576
Abstract

This report describes the clinical history and laboratory findings of three sisters with severe inherited factor VII deficiency. We present current knowledge about factor VII structure and function, and discuss clinical presentation as well as management options for patients affected by factor VII deficiency.

摘要

本报告描述了三名患有严重遗传性凝血因子Ⅶ缺乏症姐妹的临床病史和实验室检查结果。我们介绍了目前关于凝血因子Ⅶ结构和功能的知识,并讨论了凝血因子Ⅶ缺乏症患者的临床表现及治疗方案。

相似文献

1
Menorrhagia caused by severe hereditary factor VII deficiency. Case 1.严重遗传性因子VII缺乏症所致月经过多。病例1。
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2
Life-threatening menorrhagia secondary to Factor VII deficiency and leiomyomata.
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[Factor VII deficiency--case report].
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Hereditary factor VII deficiency in a Chinese family.一个中国家庭中的遗传性凝血因子VII缺乏症
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Acta Haematol. 1983;69(2):117-22. doi: 10.1159/000206867.
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[Clinical studies of familial hereditary factor VII deficiency (author's transl)].家族性遗传性因子VII缺乏症的临床研究(作者译)
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引用本文的文献

1
Reproductive health and hemostatic issues in women and girls with congenital factor VII deficiency: A systematic review.先天性因子 VII 缺乏症女性和女童的生殖健康和止血问题:系统评价。
J Thromb Haemost. 2022 Dec;20(12):2758-2772. doi: 10.1111/jth.15872.