Kohut Maciej, Marek Tomasz, Rybicka Janina, Bołdys Hubert, Nowak Andrzej, Wojtyczka Andrzej, Olakowski Marek, Graniewski Jarosław
Katedry i Kliniki Gastroenterologii, Slaskiej Akademii Medycznej w Katowicach.
Wiad Lek. 2003;56(3-4):192-8.
Authors describe a case of 24 years old woman with recurrent lower GI bleeding and mechanical obstruction. Crohn's disease was diagnosed at the beginning. It was impossible to treat the patient's profound anemia with blood transfusions due to her religion believes. The diagnosis of Peutz-Jeghers syndrome was made postoperatively. During operation mechanical obstruction (invagination of terminal ileum into ascending colon) was released. The invagination was caused by 3 cm large polyp localized in terminal ileum. Subsequently, 8 polyps (varying in size between 0.5 and 3 cm) in the small intestine were localized using intraoperative upper GI endoscopy and enteroscopy and finally surgically removed. Typical hamartomas were found on histopathological examination of removed polyps. Authors present modern attitude to Peutz-Jeghers syndrome--its diagnostics, treatment and follow-up.
作者描述了一名24岁女性,患有复发性下消化道出血和机械性肠梗阻。最初诊断为克罗恩病。由于其宗教信仰,无法通过输血治疗该患者严重的贫血。术后诊断为黑斑息肉综合征。手术中解除了机械性肠梗阻(回肠末端套入升结肠)。套叠是由位于回肠末端的一个3厘米大的息肉引起的。随后,通过术中上消化道内镜检查和小肠镜检查在小肠中发现了8个息肉(大小在0.5至3厘米之间),最终手术切除。切除息肉的组织病理学检查发现了典型的错构瘤。作者介绍了对黑斑息肉综合征的现代认识——其诊断、治疗和随访。