Giancotti Aldo, Romanini Gaia, Docimo Raffaella, Arcuri Claudio
Department of Orthodontics, Univeristy of Rome "Tor Vergata", Ospedale Fatebenefratelli, Isola Tiberina.
J Clin Pediatr Dent. 2003 Summer;27(4):377-80. doi: 10.17796/jcpd.27.4.6356k0231w213386.
Orthodontic treatment in a young patient with Beckwith-Wiedeman Syndrome (BWS) is reported and a multidisciplinary approach to the management of this syndrome is reviewed. The patient presented with a tendency to Class III malocclusion, an open-bite and a slight macroglossia, which was treated at an early age by glossotomy. It was decided to monitor growth without treatment and to wait for the best time to begin therapy. It was based only on functional rehabilitation, without any fixed appliances, in which optimum intercuspation of the teeth and the skeletal Class I relationship was achieved and maintained after the retention period of three years. In conclusion the treatment of BWS patients requires a multidisciplinary approach that includes orthodontics, orthopaedics and surgical intervention. It is also necessary to underline the significance of diagnosis at an early age and timely treatment to reduce the development of dento-skeletal alterations.
本文报道了一名患有贝克威思-维德曼综合征（BWS）的年轻患者的正畸治疗情况，并综述了该综合征的多学科管理方法。该患者表现出Ⅲ类错牙合倾向、开牙合和轻度巨舌症，早年通过舌切除术进行了治疗。决定在不进行治疗的情况下监测生长情况，并等待最佳治疗时机。治疗仅基于功能康复，未使用任何固定矫治器，在三年的保持期后实现并维持了牙齿的最佳尖窝关系和骨骼Ⅰ类关系。总之，BWS患者的治疗需要多学科方法，包括正畸、正颌和手术干预。还必须强调早期诊断和及时治疗对减少牙颌面畸形发展的重要性。
