Richards P S, Clifton A G
Department of Neuroradiology, Atkinson Morley Hospital, Wimbledon, London, UK.
J Laryngol Otol. 2003 Aug;117(8):666-9. doi: 10.1258/002221503768200075.
We present a case of a papillary tumour of the petrous bone. The established terminology for this rare neoplasm is endolymphatic sac tumour (ELST) but the true origin remains controversial. ELSTs are associated with von Hippel-Lindau disease. They are locally invasive, highly vascular and often require endovascular embolization prior to surgery. Both radiologically and histologically ELSTs are easily mistaken for other more common tumours such as paragangliomas and renal or papillary thyroid carcinoma metastases. This is important because local excision is curative.
我们报告一例岩骨乳头状肿瘤病例。这种罕见肿瘤的既定术语是内淋巴囊瘤（ELST），但其真正起源仍存在争议。ELST与冯·希佩尔-林道病相关。它们具有局部侵袭性、血管丰富，且手术前常需进行血管内栓塞。在放射学和组织学上，ELST都很容易被误诊为其他更常见的肿瘤，如副神经节瘤以及肾或甲状腺乳头状癌转移瘤。这一点很重要，因为局部切除可治愈该病。
