Bernedo N, González I, Gastaminza G, Audícana M T, Fernández E, Muñoz D
Servicio de Alergia e Inmunología, Hospital Santiago Apóstol, Spain.
J Investig Allergol Clin Immunol. 2003;13(2):137-9.
Gastrointestinal and respiratory involvement is common in hereditary angioedema, laryngeal edema being the main cause of mortality in these patients. We report the case of an 18 year-old woman with a history of hereditary angioedema, who presented an episode of coughing and vomiting the night before, and who was diagnosed with pneumomediastinum as a complication of an episode of angioedema. We review the causes and pathogenesis of the mediastinic emphysema.
胃肠道和呼吸道受累在遗传性血管性水肿中很常见,喉头水肿是这些患者死亡的主要原因。我们报告一例18岁有遗传性血管性水肿病史的女性病例,该患者前一晚出现咳嗽和呕吐发作,并被诊断为血管性水肿发作并发症所致的纵隔气肿。我们回顾纵隔气肿的病因和发病机制。