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黏多糖贮积症Ⅰ型伴阻塞性睡眠呼吸暂停继发的肺心病，采用持续气道正压通气治疗。

Hurler's syndrome with cor pulmonale secondary to obstructive sleep apnoea treated by continuous positive airway pressure.

作者信息

Chan D, Li A M, Yam M C, Li C K, Fok T F

机构信息

Department of Paediatrics, Prince of Wales Hospital, Chinese University of Hong Kong, Shatin, Hong Kong SAR, China.

出版信息

J Paediatr Child Health. 2003 Sep-Oct;39(7):558-9. doi: 10.1046/j.1440-1754.2003.00218.x.

DOI:10.1046/j.1440-1754.2003.00218.x
PMID:12969215
Abstract

A 6-year-old boy with Hurler's syndrome presented with right heart failure and pulmonary hypertension secondary to severe obstructive sleep apnoea. Both his sleep apnoea and cor pulmonale were effectively controlled with continuous positive airway pressure therapy.

摘要

一名患有黏多糖贮积症Ⅰ型（Hurler综合征）的6岁男孩因严重阻塞性睡眠呼吸暂停继发右心衰竭和肺动脉高压。他的睡眠呼吸暂停和肺源性心脏病均通过持续气道正压通气治疗得到有效控制。

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