Huang Shih-Ming, Chen Chu-Chin, Chiu Pao-Chin, Lai Ping-Hong, Ho Jih-Tsun, Tseng Hui-Hwa
Department of Pediatrics, Veterans General Hospital-Kaohsiung, National Yang-Ming University, Taiwan, Republic of China.
J Pediatr Hematol Oncol. 2003 Sep;25(9):743-6. doi: 10.1097/00043426-200309000-00014.
Chordoma is a rare and slow-growing malignant neoplasm that arises from the embryonic notochord. It is rare to see a thoracic chordoma presenting as a posterior mediastinal mass with pleural seeding in a child. The authors report a chordoma of the thoracic spine with posterior mediastinal extension and pleural seeding in a 2-year-old boy who presented with asymmetric bilateral hand temperature and lower limb paralysis. The clinical course progressed rapidly, resulting in death.
脊索瘤是一种罕见的、生长缓慢的恶性肿瘤，起源于胚胎脊索。儿童胸段脊索瘤表现为后纵隔肿块并伴有胸膜播散的情况较为罕见。作者报告了一例2岁男孩的胸椎脊索瘤，该肿瘤向后纵隔延伸并伴有胸膜播散，患儿表现为双侧手部温度不对称及下肢瘫痪。临床病程进展迅速，最终导致死亡。
