眼睑黏液性小汗腺癌。
Mucinous eccrine carcinoma of the eyelid.
作者信息
Snow S N, Reizner G T
机构信息
Department of Surgery, University of Wisconsin-Madison 53705.
出版信息
Cancer. 1992 Oct 15;70(8):2099-104. doi: 10.1002/1097-0142(19921015)70:8<2099::aid-cncr2820700815>3.0.co;2-c.
BACKGROUND
Mucinous eccrine carcinoma (MEC) is a rare malignant tumor that typically arises in the periorbital area.
METHODS
The authors report the 73rd case of primary MEC of the skin. This patient's clinicopathologic findings and the world literature are reviewed.
RESULTS
Patient ages range from 8-84 years (median, 63 years). The male-to-female ratio was approximately 2:1. The racial distribution was 67% white, 32% black, and 4% Asian. Primary MEC originates in the head and neck region in approximately 75% of patients. The most common location was the periorbital area (40% or 29 of 73 patients). The local recurrence rate after conventional surgery was: eyelid, 34%; scalp, 36%; and face, 33%.
CONCLUSIONS
Primary MEC is often a slow-growing tumor that may recur after traditional surgical excision. Recurrent eyelid MEC tends to be locally destructive with a regional metastatic rate of 3.5% (1 of 29). The regional metastatic rate for all sites was 11%, and the distant metastatic rate was 3%.
背景
黏液性小汗腺癌（MEC）是一种罕见的恶性肿瘤，通常发生于眶周区域。
方法
作者报告了第73例原发性皮肤MEC病例。对该患者的临床病理特征及世界文献进行了回顾。
结果
患者年龄范围为8 - 84岁（中位数为63岁）。男女比例约为2:1。种族分布为67%为白人，32%为黑人，4%为亚洲人。约75%的患者原发性MEC起源于头颈部区域。最常见的部位是眶周区域（73例患者中有40%即29例）。传统手术后的局部复发率为：眼睑，34%；头皮，36%；面部，33%。
结论
原发性MEC通常是一种生长缓慢的肿瘤，传统手术切除后可能复发。复发性眼睑MEC往往具有局部破坏性，区域转移率为3.5%（29例中的1例）。所有部位的区域转移率为11%，远处转移率为3%。
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