Sung D F
Department of Surgery, Provincial Hospital-Tsin Chu.
Zhonghua Yi Xue Za Zhi (Taipei). 1992 Sep;50(3):261-5.
Fibromatosis is often found in the anterior abdominal wall of parous women. It occurs rarely in the chest wall and is rarely found in children. Our case was a 7-year-old male patient with a rapid-growing, painless tumor in the right anterior chest wall for 6 months. He received a resection of the tumor, the bilateral clavicular heads, the upper-third of the sternum and segments of the first and second ribs bilaterally. Reconstruction was conducted by transposition of the pectoralis major muscle and a prosthesis of wire mesh with methyl methacrylate. Histologically, the tumor showed dense collagenous tissue consistent with mature aggressive fibromatosis. It was a benign tumor without distant metastatic potential but with an aggressive clinical behavior. Although postoperative radiotherapy is usually indicated in adults, it was reserved due to the immature skeleton of this boy. In this case, the use of a rigid prosthesis avoided tracheostomy and postoperative ventilation.
纤维瘤病常见于经产妇的前腹壁。它很少发生在胸壁，在儿童中也很少见。我们的病例是一名7岁男性患者，右前胸壁有一个生长迅速、无痛的肿瘤，病程6个月。他接受了肿瘤切除，双侧锁骨头部、胸骨上三分之一以及双侧第一和第二肋骨部分切除。通过胸大肌移位和带甲基丙烯酸甲酯的金属丝网假体进行重建。组织学上，肿瘤显示致密的胶原组织，符合成熟的侵袭性纤维瘤病。这是一种良性肿瘤，无远处转移潜能，但具有侵袭性的临床行为。虽然成人术后通常需要放疗，但由于该男孩骨骼未成熟，未进行放疗。在本病例中，使用刚性假体避免了气管切开术和术后通气。
