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[Hypothalamic hypopituitarism with hyperphagia and subacute dementia due to neurosarcoidosis: case report and literature review].

作者信息

Vanhoof J, Wilms G, Bouillon R

机构信息

Universitair Zieknhuis Gasthuisberg, Leuven, Belgie.

出版信息

Acta Clin Belg. 1992;47(5):319-28. doi: 10.1080/17843286.1992.11718250.

DOI:10.1080/17843286.1992.11718250
PMID:1334320
Abstract

The frequency of neurologic involvement in sarcoidosis is about 5%. When the clinical picture presents with only neurological manifestations, as it did in our patient, the diagnosis at presentation is often difficult. Involvement of other tissues must therefore be actively searched. We describe a case of neurosarcoidosis, presenting with hypothalamic hypopituitarism, progressive loss of visual fields, subacute dementia and hypothalamic hyperphagia. The disease very well responded to high dose corticosteroids. The pathology, diagnostic procedures, prognosis and treatment of neurosarcoidosis are discussed.

摘要

相似文献

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Acta Clin Belg. 1992;47(5):319-28. doi: 10.1080/17843286.1992.11718250.
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Sarcoidosis presenting as late-onset dementia.以迟发性痴呆为表现的结节病。
J Neurol. 1996 Jun;243(6):484-7. doi: 10.1007/BF00900506.