Telander R L, Lennox C, Sieber W
Mayo Clin Proc. 1976 Sep;51(9):578-84.
Nine cases of sequestration of the lung were seen in children. Bronchopulmonary sequestration of the lung is a distinct congenital anomaly and clinical entity that can be distinguished from other congenital abnormalities of the lung. Such a congenital anomaly must be considered in children who, on roentgenologic examination, are found to have an opacity in the lower lung fields. Intralobar bronchopulmonary sequestration often is associated with recurrent pulmonary sepsis, whereas extralobar sequestration is less likely to be symptomatic and usually exhibits no abnormal physical findings. In a unique case, we found an extralobar sequestration associated with an esophageal duplication that communicated with the sequestered lobe but not with the esophagus. This situation represents a transitional stage in embryonic development of extralobar sequestration. Intralobar and extralobar forms of sequestration show many common characteristics indicating a common embryogenesis. Surgical excision, consisting of lobectomy or segmentectomy, is safe and effective and may be accomplished without morbidity or mortality.
儿童中发现9例肺隔离症。肺支气管肺隔离症是一种独特的先天性异常和临床实体，可与其他先天性肺异常相鉴别。对于经X线检查发现下肺野有不透明区的儿童，必须考虑这种先天性异常。叶内型支气管肺隔离症常与反复肺部感染有关，而叶外型隔离症较少出现症状，通常无异常体征。在一个独特病例中，我们发现一叶外型隔离症与食管重复畸形相关，该重复畸形与隔离肺叶相通但与食管不相通。这种情况代表了叶外型隔离症胚胎发育的一个过渡阶段。叶内型和叶外型隔离症有许多共同特征，提示有共同的胚胎发生。手术切除，包括肺叶切除术或肺段切除术，安全有效，且可在无并发症或死亡率的情况下完成。
