Sankalé A A, Fall I, Ndoye M, Diop A
Clinique Chirurgicale CHU de Dakar.
Dakar Med. 1992;37(2):131-6.
Eight cases of uretero-pelvic junction syndrom collected in the ten past years are reported. They are 4 males and 4 females ranged from 18 months to 15 years with a mean age of 4.5 years. This age too late is probably due to the misknowlege but also to the lack of information about the pathology. The main characteristics of this syndrome are analysed according to the literature. All patients except one underwent nephrectomy because the irreverible lesions of the kidney. The authors emphasize the importance of early diagnosis done by antenatal echography but it can be made with a good clinical examination followed by the results of I.V.P. It is necessary for them to make parents, general practitioners and paediatricians sensitive to that pathology to avoid such operating act whose consequence are very serious where as it is benign.
报告了过去十年间收集的8例输尿管肾盂连接部综合征病例。其中男性4例,女性4例,年龄从18个月至15岁不等,平均年龄4.5岁。这个年龄偏大可能是由于认识不足,也可能是由于缺乏关于该病理学的信息。根据文献分析了该综合征的主要特征。除1例患者外,所有患者均因肾脏不可逆病变而接受了肾切除术。作者强调产前超声检查进行早期诊断的重要性,但也可通过良好的临床检查并结合静脉肾盂造影结果做出诊断。有必要让家长、全科医生和儿科医生对这种病理学有所认识,以避免进行后果非常严重的此类手术,而实际上它是良性的。