Noonan J A, Srivastava T N, Trinkle J K, Castellos J M
Chest. 1976 Nov;70(5):683-5. doi: 10.1378/chest.70.5.683.
A large patent ductus arteriosus associated with total anomalous pulmonary venous return results in a unique hemodynamic pattern, and long-term survival has been rare. Two patients, aged five and 18 years, underwent successful surgical repair of supracardiac total anomalous pulmonary venous return and an associated large patent ductus arteriosus. The association of the Noonan syndrome in the 18-year-old woman is of additional interest.
与完全性肺静脉异位引流相关的大型动脉导管未闭会导致独特的血流动力学模式,长期存活情况罕见。两名患者,年龄分别为5岁和18岁,接受了心上型完全性肺静脉异位引流及相关大型动脉导管未闭的成功手术修复。18岁女性患者合并努南综合征这一情况更具研究价值。