Calmettes C, Rosenberg-Gourgin M, Caron J, Feingold N
CHU St. Antoine, Paris, France.
Henry Ford Hosp Med J. 1992;40(3-4):276-7.
Pheochromocytoma is a frequent indicator of multiple endocrine neoplasia type 2A (MEN 2A); in the 35 French MEN 2A families in which a pheochromocytoma occurred first in some affected members, 30% of the patients had a pheochromocytoma as the first manifestation constituting 45% of all patients with pheochromocytomas. The finding of a pheochromocytoma is a strong indication for a search for medullary thyroid carcinoma and for initiating family screening.
嗜铬细胞瘤是2A型多发性内分泌腺瘤病（MEN 2A）的常见指标；在35个法国MEN 2A家系中，部分受累成员首先出现嗜铬细胞瘤，30%的患者以嗜铬细胞瘤为首发表现，占所有嗜铬细胞瘤患者的45%。发现嗜铬细胞瘤强烈提示需筛查甲状腺髓样癌并启动家系筛查。
