成人型戈谢病：1例组织化学研究（作者译）
[Adult-type Gaucher's disease: an histochemical study of one case (author's transl)].
作者信息
Lageron A, Polonovski J
出版信息
Acta Histochem. 1976;57(1):157-64.
PMID:137645
Abstract
Spleen of adult-type Gaucher's disease has been investigated by histochemical technics. As usually, an overload of cerebroside (revealed by the PAS reaction for glycolipids) with beta-glucosidase deficiency has been demonstrated. But many particularities must be emphasized in this case: increase of acid MPS, high activities of pentose pathway--and glycolysis enzymes in the overload cells.
摘要
采用组织化学技术对成人型戈谢病的脾脏进行了研究。通常情况下，已证实存在脑苷脂过载（通过糖脂的PAS反应显示）以及β-葡萄糖苷酶缺乏。但在这种情况下必须强调许多特殊之处：酸性黏多糖增加，过载细胞中戊糖途径及糖酵解酶的活性较高。
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Acta Histochem. 1976;57(1):157-64.
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Histoenzymological activities of Gaucher cells.戈谢细胞的组织酶学活性。
J Inherit Metab Dis. 1981;4(2):75-6. doi: 10.1007/BF02263598.
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