Roccatagliata G, Albano C
Riv Neurol. 1976 Jul-Aug;46(4):297-332.
The scope of the work is to list and analyse, after a historical introduction on the subject, the principle clinical characteristics of "Huntington's Disease". The epidemiological aspects, those clinical-semeiotical, the course of the disease and the type of after affects of Huntington's Diseases are examined. The more significant details of the natural history of the chorea maior, as emerge from the literature, are compared with those that result from the study of the thirty cases of this chronic disease. In particular the following are analysed, the genetic aspects, the character of the psycho-organic deterioration of the chronic chorea, the psychiatric component and various clinical-semeiotical formalities, how the disease begins, its course, its duration, etc. The authors conclude pointing out the particular character of the dementia of Huntington's Disease, (of the pre-frontal type), the strong psychopathological incidence and the particular formalities of hereditary transmission of the mendelian type of this singular disease.
这项工作的范围是，在对该主题进行历史介绍之后，列出并分析“亨廷顿舞蹈症”的主要临床特征。研究了其流行病学方面、临床症状、疾病进程以及亨廷顿舞蹈症的后遗症类型。将文献中出现的大舞蹈病自然史的更重要细节与对该慢性病30例病例研究的结果进行比较。特别分析了以下内容：遗传方面、慢性舞蹈病心理器质性衰退的特征、精神科成分以及各种临床症状表现形式、疾病如何开始、其进程、持续时间等。作者在结论中指出了亨廷顿舞蹈症痴呆症（前额叶型）的特殊特征、强烈的精神病理学影响以及这种独特疾病孟德尔式遗传的特殊形式。
