Nakamura T, Miwa K, Kanda S, Nonaka K, Anan H, Higash S, Beppu K
Kyushu University, Fukuoka, Japan.
Dentomaxillofac Radiol. 1992 Feb;21(1):45-9. doi: 10.1259/dmfr.21.1.1397452.
The radiographic features of the jaws in the mucopolysaccharidoses and related disorders (MPS) have been reviewed and three further cases are reported here, with particular reference to a novel dental anomaly, not previously described in detail, in two of them. The dental changes appear to be fully developed by the third decade and are characterized by bilateral multiple impacted molar teeth, which conglomerate in a single follicle to form a characteristic rosette of teeth. Rosetting was present only in relatively mature cases of MPS. However, it was also seen in the fourth patient, where we could not detect any other abnormal clinical or radiographic features. We therefore propose that since multiple rosetting of molar teeth can also occur in an isolated form, it is only suggestive of MPS.
对黏多糖贮积症及相关疾病（MPS）患者颌骨的影像学特征进行了综述，并报告了另外3例病例，特别提及其中2例出现了一种此前未详细描述的新型牙齿异常。牙齿变化似乎在第三个十年时已完全显现，其特征为双侧多个阻生磨牙，这些磨牙聚集在单个牙囊中，形成特征性的牙玫瑰花结。牙玫瑰花结仅在相对成熟的MPS病例中出现。然而，在第4例患者中也观察到了这种情况，在该患者中我们未检测到任何其他异常的临床或影像学特征。因此，我们提出，由于磨牙的多个牙玫瑰花结也可能以孤立形式出现，所以它仅提示可能患有MPS。
