Collan Y, Pesonen E
Helv Paediatr Acta. 1977 Apr;31(6):521-6.
A baby born with cardiac, cerebral, ocular, palatal, renal and pulmonary anomalies died four hours after birth. The cardiac anomaly consisted of a double outlet right ventricle with extreme hypertrophy of the muscle bundles associated with the crista supraventricularis. The hypertrophic muscle mass divided the right ventricle into two parts, one of them corresponding to the outflow tract of the pulmonary artery. The other part received blood from the left ventricle through a septal defect and led the flow into the aorta. The two compartments were connected by a narrow canal at the apex of the right ventricle. Blood flow into the pulmonary artery was strictly dependent on the patency of the ductus arteriosus. Signs of closure could be found on the inner surface of the duct.
一名患有心脏、大脑、眼睛、腭、肾脏和肺部畸形的婴儿出生后四小时死亡。心脏畸形包括右心室双出口，伴有与室上嵴相关的肌束极度肥大。肥厚的肌肉团将右心室分为两部分，其中一部分对应肺动脉流出道。另一部分通过室间隔缺损从左心室接收血液，并将血流导入主动脉。这两个腔室在右心室顶端通过一条狭窄的管道相连。流入肺动脉的血流严格依赖动脉导管的通畅。在导管内表面可发现闭合的迹象。
