Double outlet right ventricle with extreme hypertrophy of muscle bundles associated with crista supraventricularis. A heart with three ventricles.

A baby born with cardiac, cerebral, ocular, palatal, renal and pulmonary anomalies died four hours after birth. The cardiac anomaly consisted of a double outlet right ventricle with extreme hypertrophy of the muscle bundles associated with the crista supraventricularis. The hypertrophic muscle mass divided the right ventricle into two parts, one of them corresponding to the outflow tract of the pulmonary artery. The other part received blood from the left ventricle through a septal defect and led the flow into the aorta. The two compartments were connected by a narrow canal at the apex of the right ventricle. Blood flow into the pulmonary artery was strictly dependent on the patency of the ductus arteriosus. Signs of closure could be found on the inner surface of the duct.