[伴有氨基酸尿症和糖尿症的肝糖原生成。临床与生化研究] - Suppr

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超能文献

[GLYCOGENOSIS OF THE LIVER WITH AMINOACIDURIA AND GLYCOSURIA. CLINICAL AND BIOCHEMICAL STUDIES].

作者信息

ROTTHAUWE H W, FICHSEL H, HELDT H W, KIRSTEN E, REIM M, SCHMIDT E, SCHMIDT F W, WESEMANN W

出版信息

Klin Wochenschr. 1963 Aug 15;41:818-25. doi: 10.1007/BF01789076.

DOI:10.1007/BF01789076

PMID:14045596

Abstract

摘要

相似文献

[GLYCOGENOSIS OF THE LIVER WITH AMINOACIDURIA AND GLYCOSURIA. CLINICAL AND BIOCHEMICAL STUDIES].[伴有氨基酸尿症和糖尿症的肝糖原生成。临床与生化研究]

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Hepatomegaly and abnormal liver tests due to glycogenosis in adults with diabetes.糖尿病成人患者因糖原贮积症导致肝肿大及肝功能检查异常。

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AN ELECTRON MICROSCOPIC AND BIOCHEMICAL STUDY OF TYPE II GLYCOGENOSIS.II型糖原贮积病的电子显微镜及生化研究

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Liver phosphorylase deficiency in glycogenosis type VI: documentation by biochemical analysis of hepatic biopsy specimens.糖原贮积症VI型中的肝磷酸化酶缺乏症：通过肝活检标本的生化分析进行记录

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[CONTRIBUTION TO THE CLINICAL PICTURE OF GLYCOGENOSIS WITH AMINOACIDURIA IN SIBLINGS].[对伴有氨基酸尿症的糖原累积病在同胞中的临床症状的贡献]

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[Hepatic glycogenoses. Correlations between the clinical and biochemical characteristics and the type of enzymatic deficiency: glucose-6-phosphatase, amylo-1-6-glucosidase, phosphorylase].[肝糖原贮积症。临床和生化特征与酶缺乏类型（葡萄糖-6-磷酸酶、淀粉-1,6-葡萄糖苷酶、磷酸化酶）之间的相关性]

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[BRAIN DAMAGE AND ENZYMATIC ACTIVITIES IN BODY FLUID].[体液中的脑损伤与酶活性]

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Enzyme localization in proteins separated by paper electrophoresis in human seminal plasma.人类精浆中经纸电泳分离的蛋白质的酶定位

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Diabetes-like renal glomerular disease in Fanconi-Bickel syndrome.范科尼-比克综合征中的糖尿病样肾小球疾病。

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[Debré-De Toni-Fanconi syndrome with glycogenosis of the liver].[伴有肝糖原贮积症的德布雷-德托尼-范科尼综合征]

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Fanconi-Bickel syndrome.范科尼-比克综合征

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Type I glycogen storage disease: kidney involvement, pathogenesis and its treatment.I型糖原贮积病：肾脏受累、发病机制及其治疗

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Incidence of glycogen storage disease in the German Federal Republic.德意志联邦共和国糖原贮积病的发病率。

Z Kinderheilkd. 1975 Aug 11;120(2):79-85. doi: 10.1007/BF00445157.

本文引用的文献

[Chronic aminoaciduria (amino acid diabetes or nephrotic-glucosuric dwarfism) in glycogen storage and cystine disease].[糖原累积病和胱氨酸病中的慢性氨基酸尿症（氨基酸糖尿病或肾性糖尿侏儒症）]

Helv Paediatr Acta. 1949 Nov;4(5):359-96.

Glucose-6-phosphatase deficiency glycogen storage disease. Studies on the interrelationships of carbohydrate, lipid, and purine abnormalities.葡萄糖-6-磷酸酶缺乏性糖原贮积病。碳水化合物、脂质和嘌呤异常之间相互关系的研究。

Pediatrics. 1962 Apr;29:553-65.

[Glycogenosis caused by deficiency of hepatic phosphorylase].[肝磷酸化酶缺乏引起的糖原贮积症]

Arch Fr Pediatr. 1960;17:14-37.

The interconversion of glutamic acid and aspartic acid in respiring tissues.呼吸组织中谷氨酸和天冬氨酸的相互转化。

Biochem J. 1960 Jun;75(3):523-9. doi: 10.1042/bj0750523.

[On the metabolite content and the metabolite concentration in the liver of the rat].[关于大鼠肝脏中的代谢物含量及代谢物浓度]

Biochem Z. 1959;332:18-46.

[PHOSPHATE-CONTAINING METABOLITES IN ANION-EXCHANGE CHROMATOGRAMS OF ACID-SOLUBLE EXTRACTS FROM RAT LIVER IN THE NANO AREA].[纳米区域大鼠肝脏酸溶性提取物阴离子交换色谱图中的含磷酸盐代谢物]

Biochem Z. 1963 Jul 10;337:397-413.

The pathway of glutamate oxidation by mitochondria isolated from different tissues.从不同组织分离得到的线粒体对谷氨酸的氧化途径。

Biochim Biophys Acta. 1962 Feb 26;57:256-69. doi: 10.1016/0006-3002(62)91119-8.

Liver enzymes in glycogen storage disease.糖原贮积病中的肝脏酶

Metabolism. 1960 Oct;9:880-3.

Free amino acids in alloxan diabetic rat livers.四氧嘧啶糖尿病大鼠肝脏中的游离氨基酸

Biochem Biophys Res Commun. 1961 Mar 10;4:169-74. doi: 10.1016/0006-291x(61)90264-9.

Steady state equilibria of some DPN-linked reactions and the oxidation/reduction state of the DPN/DPNH system in the cytoplasmatic compartment of liver cells in vivo.体内肝细胞胞质区室中一些与二磷酸吡啶核苷酸（DPN）相关反应的稳态平衡以及DPN/二磷酸吡啶核苷酸还原型（DPNH）系统的氧化/还原状态

Biochem Biophys Res Commun. 1961 Mar 10;4:159-62. doi: 10.1016/0006-291x(61)90262-5.

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