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腭肌阵挛中不同运动子系统的振荡活动。病例报告。

Oscillatory activity in different motor subsystems in palatal myoclonus. A case report.

作者信息

Hefter H, Logigian E, Witte O W, Reiners K, Freund H J

机构信息

Department of Neurology, University of Düsseldorf, Germany.

出版信息

Acta Neurol Scand. 1992 Aug;86(2):176-83. doi: 10.1111/j.1600-0404.1992.tb05062.x.

DOI:10.1111/j.1600-0404.1992.tb05062.x
PMID:1414229
Abstract

In a patient with palatal myoclonus the mutual interaction between voluntary movements and the myoclonic activity was analysed. Amplitude and frequency of myoclonic activity in hand muscles were modulated by flexions and extensions. A 1:1 relationship was found between EMG-bursts in hand muscles and palatal movements. A 1:2 relationship was found between eye and finger movements. Resetting of myoclonus in the abductor digiti minimi muscle occurred after cutaneous ulnar nerve stimulation. It is suggested that feedback plays an important role in the generation of the oscillatory activity in PM in addition to pacemaker activity in brainstem neurons.

摘要

对一名患有腭肌阵挛的患者,分析了自主运动与肌阵挛活动之间的相互作用。手部肌肉肌阵挛活动的幅度和频率受屈伸动作调节。发现手部肌肉的肌电图爆发与腭部运动之间存在1:1的关系。发现眼部和手指运动之间存在1:2的关系。尺神经皮肤刺激后,小指展肌的肌阵挛发生重置。研究表明,除了脑干神经元的起搏器活动外,反馈在腭肌阵挛振荡活动的产生中也起着重要作用。

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